A frequência da Anomalia de Ebstein encontrada foi semelhante a de outros Centros. A técnica de Cone foi viável na maior parte dos pacientes. A mortalidade. Ebstein’s anomaly is a malformation of the tricuspid valve. In this defect, there is a downward displacement of the tricuspid valve (located between the upper and. Antecedentes: en la actualidad, con la ecocardiografía fetal, es pos ble confirmar el diagnóstico in utero de la anomalía de Ebstein y determinar, con certeza.

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Differential diagnosis The major differential diagnosis, particularly during fetal life, is dysplasia of the leaflets of the tricuspid valve. Patients with severe forms of the disease, particularly those presenting during the fetal period or as neonates, have an increased risk of death due to cardiac failure, including at birth or during physical exercise. Mean cardiothoracic index was 0.

Ebstein’s Anomaly | Stanford Health Care

anoalia Cardiothoracic index, echocardiographic findings, surgical indications, surgery performed and early post-operative evaluation. Medical treatment relies on inotropic agents in case of cardiac failure and antiarrhythmic drugs in case of tachyarrhythmia.

The indications for surgery were: Ebstein’s anomaly in children: Ebstein’s Anomaly congenital heart defect ebsteins-anomaly. J Am Coll Cardiol, 3pp.


ebstdin Data on X-ray, echocardiography, indications for surgery, type of surgical techniques and complications are presented in Table 2. Disease definition Ebstein’s malformation is a rare congenital cardiac anomaly characterized by rotational displacement of the septal and inferior leaflets of the tricuspid valve such that they are hinged within the right ventricle, rather than as expected at the atrioventricular junction.

Anomalía de Ebstein en niños

Access to health care services are still a serious problem in our continent, from the prenatal period to old age, which is why we have a small sample without neonates with severe forms of EA and older patients with good functional status.

Ebstein’s anomaly in a patient with Down’s syndrome.

We analyzed all patients diagnosed with congenital heart defects. Am J Med Genet A,pp.

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Ebstein’s anomaly is a rare complex congenital heart defect of the tricuspid valve. The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis ebdtein diagnosis or treatment.

dr Those with severe forms can present at various ages with arrhythmias, cyanosis, and sometimes cardiac failure. Cardiol Young, 14pp. It is usually associated with an atrial septal defect.


The malformation is often associated with other cardiac lesions, such as atrial or ventricular septal defects, patency of the arterial duct, and pulmonary stenosis. Data on clinical presentation, chest X-ray, electrocardiography, echocardiographic studies and surgical reports were analyzed.

Resultados Foram analisados ecocardiogramas sequenciais.

This study revealed that 0. Cardiol Young, 16pp. Ventricular septal defect in children and adolescents in CR was performed in the majority of patients with excellent immediate and short-term results. Demographic data, clinical presentations, and NYHA functional class of the study population are shown in Table 1.

Valdano Manuel a.

Ebstein’s anomaly in children: A single-center study in Angola | Revista Portuguesa de Cardiologia

Bol Asoc Med P Anomxlia ; Clinical and echocardiographic features of Ebstein’s malformation in Sudanese patients. Br Heart J ; Fetal Diagn Ther ; The authors have no conflicts of interest to declare. In these patients, the mean bypass time was However, the technique could not be applied in two patients for the reasons described above.